Bleeding Disorders Notes

Table of Contents(toc)


Prolonged PT (extrinsic pathway factors):

  • Inherited: Factor VII deficiency
  • Acquired: mild vitamin K deficiency, Liver disease, warfarin

Prolonged aPTT (intrinsic pathway factors):

  • Inherited: 
    • factors VIII, IX, XI deficiency; 
    • factor XII, 
    • Prekallikrein or HMW kininogen deficiency
    • Von Willebrand disease
  • Acquired: 
    • Heparin, 
    • lupus anticoagulant, 
    • acquired Von Willebrand disease

Prolonged PT and Prolonged aPTT (common pathway factors):

  • Inherited: 
    • Prothrombin (II), 
    • Fibrinogen (I),
    •  factor V and factor X deficiencies
  • Acquired: 
    • DIC, 
    • severe liver disease, 
    • severe vitamin K deficiency, 
    • Direct thrombin inhibitor – agratroban, 
    • dabigatran, 
    • Direct factor Xa inhibitor – rivaroxaban, apixaban, edoxaban,  fondaparinaux

Q. In a patient with normal CBC findings with raise in PTT, what could be the diagnosis?

a) Hemophilia

b) ITP

c) Von-willebrand diease

d) Aplastic anemia

Answer is : A

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